Suprasellar Germinoma
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Suprasellar tumor arising from germ cells
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Vision loss is caused by compression
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Teenagers are most at risk
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No sex predominance
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Often cured by chemotherapy and radiation therapy
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Core clinical features
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Subacute or chronic vision loss
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Hemianopic visual field defects
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Optic discs appear normal or pale
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Afferent pupil defect
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Possible accompanying clinical features
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Hypopituitarism, especially diabetes insipidus
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Dorsal midbrain syndrome from a pineal region germinoma
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Imaging features
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Suprasellar mass that enhances avidly
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Pineal mass often also present
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Tumor deposits in cauda equina sometimes present (“dropped metastases”)
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Other masses in sellar region
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Arachnoid cyst
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Epidermoid cyst
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Langerhans cell histiocytosis
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Sphenoid sinusitis or mucocele
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Lymphocytic hypophysitis
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Pituitary abscess
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Multiple sclerosis
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Neuromyelitis optica
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Sarcoidosis
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Spine MRI will be performed to exclude dropped metastases
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Lumbar puncture will be performed to detect markers of nongerminomatous germ cell tumors
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Biopsy of the lesion will be performed if imaging is not distinctive
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Platinum-based chemotherapy is sometimes followed by low-dose brain radiation therapy
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Permanent cure will occur in >90% with minimal or no lingering neurologic deficits
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Visual recovery depends on how much damage has occurred before treatment began