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Congenital Ocular Muscle Disorders
Dissociated Vertical Deviation
What is it?
Disorder of vertical ocular alignment of uncertain origin with onset at birth or in early childhood
Isolated ocular abnormality or accompanied by infantile esotropia, latent nystagmus, and amblyopia
No diplopia
What does it look like?
Eyes usually aligned if both eyes have an unobscured view
Affected eye drifts slowly upward and outward if its view is obscured and returns to a normal position when its view is no longer obscured
May affect one eye
May affect both eyes
During the cover test, neither eye refixates with an upward movement, differentiating this condition from other forms of ocular misalignment
In some cases, one eye drifts upward under normal viewing conditions
What else looks like it?
Overaction of the inferior oblique muscles
Acquired vertical misalignment of many causes
What should you do?
Look for the characteristic slow ocular downward movement during the cover tests
Tip:
the clue to diagnosis is the absence of an upward refixational movement, which would occur in all other forms of vertical ocular misalignment
What will happen?
Patients do not have diplopia, so the main issue is the blemish of an upward drift of one affected eye
Surgical weakening of the superior rectus muscle in the drifting eye may be effective
Trap:
patients are often misdiagnosed as having a condition causing acquired ocular misalignment and subjected to unnecessary investigations
Congenital Ocular Motor Disorders
Duane Syndrome
Dissociated Vertical Deviation
Overaction of Inferior Oblique Muscles